J. Corbin Norton
Department of Urology, University of Arkansas for Medical Sciences
Amrit Singh, MD
Department of Pathology, University of Arkansas for Medical Sciences / Arkansas Children’s Hospital
Laura L. Hollenbach, MD
Department of Obstetrics and Gynecology, University of Arkansas for Medical Sciences
Georgia Gamble, MD
Department of Obstetrics and Gynecology, University of Arkansas for Medical Sciences
Laura A. Gonzalez-Krellwitz, MD
Department of Pathology, University of Arkansas for Medical Sciences / Arkansas Children’s Hospital
Stephen J. Canon, MD
Department of Pediatric Urology, Arkansas Children’s Hospital
The patient in this case is a 15-year-old female who presented with primary amenorrhea and who on work-up was found to have complete androgen insensitivity syndrome. Here, Dr. Canon at the University of Arkansas for Medical Sciences performs a prophylactic laparoscopic bilateral gonadectomy to reduce her future risk for intra-abdominal testicular malignancies. Final pathology results showed a rare case of bilateral germ cell neoplasia in situ and bilateral paratesticular leiomyomas and reinforced the decision to intervene early allowing for the removal of the gonads prior to their conversion to formal germ cell tumors.